Size
100µg
Storage Conditions
PBS with 0.02% sodium azide and 50% glycerol pH 7.3, -20℃ for 12 months (Avoid repeated freeze / thaw cycles.)
Applications
ELISA, WB, IHC
Target
SGSH
Research Area
Metabolism
Form
liquid
Recomended Dilution
WB: 1:500 - 1:2000
Type Clonality
polyclonal
Immunogen
N-sulfoglucosamine sulfohydrolase
Minimum Purity
≥95% as determined by SDS-PAGE
Synonyms
N-sulphoglucosamine sulphohydrolase|Sulfoglucosamine sulfamidase|Sulphamidase|SGSH|HSS
Host
Rabbit
UniProt ID
P51688
Gene ID
6448
Purification
Immunogen affinity purified
Iso type
IgG
Reactivity
Human, Mouse, Rat
Observed MW
57 kDa
Background
This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from imp