Size
100µg
Storage Conditions
PBS with 0.02% sodium azide and 50% glycerol pH 7.3, -20℃ for 12 months(Avoid repeated freeze / thaw cycles.)
Applications
ELISA, WB
Target
MMACHC
Research Area
Signal Transduction, Metabolism
Form
liquid
Recomended Dilution
WB: 1:500-1:2000
Type Clonality
polyclonal
Immunogen
methylmalonic aciduria(cobalamin deficiency) cblC type, with homocystinuria
Minimum Purity
≥95% as determined by SDS-PAGE
Synonyms
Cyanocobalamin reductase / alkylcobalamin dealkylase|Alkylcobalamin:glutathione S-alkyltransferase|CblC|Cyanocobalamin reductase (cyanide-eliminating)|Methylmalonic aciduria and homocystinuria type C protein (MMACHC)|MMACHC
Host
Rabbit
UniProt ID
Q9Y4U1
Gene ID
25974
Purification
Immunogen affinity purified
Iso type
IgG
Reactivity
Human, Mouse, Rat
Observed MW
32 kDa
Background
Catalyzes the reductive dealkylation of cyanocobalamin to cob(II)alamin, using FAD or FMN as cofactor and NADPH as cosubstrate(PubMed:19700356, PubMed:21697092, PubMed:22642810). Can also catalyze the glutathione-dependent reductive demethylation of methy