Información del producto
Información adicional
Storage Conditions
PBS with 0.02% sodium azide and 50% glycerol pH 7.4. Store at -20°C. Avoid repeated freeze-thaw cycles.
Applications
WB, IF
Concentration
1mg/mL
Recomended Dilution
WB 1:1,000
Type Clonality
Polyclonal
Immunogen
Recombinant Protein
Iso type
IgG
Tissue Source
Rabbit
Reactivity
Human, Rat, Mouse
Human Gen
2271
Observed Band
50kDa
Other Name
Fumarase, fumarate hydratase, HLRCC, LRCC, MCL, MCUL1
Background
Fumarase (FH) is an enzyme that catalyzes the reversible hydration/dehydration of fumarate to malate in the mitochondria. Fumarase deficiency is caused by a mutation in the fumarase gene in humans. Fumarase deficiency is one of the few known deficiencies