Size
100µg
Storage Conditions
PBS with 0.02% sodium azide and 50% glycerol pH 7.3, -20℃ for 12 months (Avoid repeated freeze / thaw cycles.)
Applications
ELISA, WB, IHC
Target
L2HGDH
Research Area
Metabolism
Form
liquid
Recomended Dilution
WB: 1:500 - 1:2000
Type Clonality
polyclonal
Immunogen
L-2-hydroxyglutarate dehydrogenase
Minimum Purity
≥95% as determined by SDS-PAGE
Synonyms
L-2-hydroxyglutarate dehydrogenase, mitochondrial|Duranin|L2HGDH|C14orf160
Host
Rabbit
UniProt ID
Q9H9P8
Gene ID
79944
Purification
Immunogen affinity purified
Iso type
IgG
Reactivity
Human, Mouse
Observed MW
40 kDa
Background
This gene encodes L-2-hydroxyglutarate dehydrogenase, a FAD-dependent enzyme that oxidizes L-2-hydroxyglutarate to alpha-ketoglutarate in a variety of mammalian tissues. Mutations in this gene cause L-2-hydroxyglutaric aciduria, a rare autosomal recessive