Size
100µg
Storage Conditions
PBS with 0.02% sodium azide and 50% glycerol pH 7.3, -20℃ for 12 months (Avoid repeated freeze / thaw cycles.)
Applications
ELISA, WB, IHC
Target
FAH
Research Area
Metabolism
Form
liquid
Recomended Dilution
WB: 1:500 - 1:2000
Type Clonality
polyclonal
Immunogen
fumarylacetoacetate hydrolase (fumarylacetoacetase)
Minimum Purity
≥95% as determined by SDS-PAGE
Synonyms
Fumarylacetoacetase (FAA)|Beta-diketonase|Fumarylacetoacetate hydrolase|FAH
Host
Rabbit
UniProt ID
P16930
Gene ID
2184
Purification
Immunogen affinity purified
Iso type
IgG
Reactivity
Human, Mouse, Rat
Observed MW
46 kDa
Background
This gene encodes the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT).